Clinical presentations of cystic fibrosis in adulthood

Abstract

Medical care for individuals with cystic fibrosis has resulted in dramatic improvement in survival and subsequently a significant change in the epidemiology of cystic fibrosis, bringing new challenges for patients and professionals. With an increasing number of patients reaching adult age, the impact of nutritional compromise and chronic infl ammation on diff erent organ systems has become increasingly manifest. The potential long term eff ect of medical interventions and therapies in early life, which aim to avoid, minimize or delay complications that occur later in life, should be considered as part of the strategies infl uencing the patient quality of life and long vitality.